HUGE RENAL ANGIOMYOLIPOMA (AML) IN TUBEROUS SCLEROSIS COMPLEX (TSC) WHICH IS CONTROLED BY EVEROLIMUS: A CASE REPORT
نویسندگان
چکیده
منابع مشابه
Everolimus for renal angiomyolipoma in tuberous sclerosis.
In The Lancet, John Bissler and colleagues report the fi rst randomised, double-blind, placebo-controlled, phase 3 trial of everolimus, an inhibitor of mammalian target of rapamycin (mTOR), in patients with tuberous sclerosis complex or sporadic lymphangioleiomyomatosis, and angiomyolipoma. Their fi ndings suggest a clear advantage for everolimus over placebo in reducing angiomyolipoma volume w...
متن کامل[Renal angiomyolipoma in a patient with tuberous sclerosis. Case report.]
OBJECTIVE To assess the importance of management and close follow-up of patients with tuberous sclerosis that associate renal angiomyolipomas. METHODS To report a case. RESULTS A 55 years old men with tuberous sclerosis diagnosed in childhood and later finding of bilateral giant renal masses in imaging studies, with significant compromise of renal function. The patient did not have a proper...
متن کاملFamilial genetic tuberous sclerosis complex associated with bilateral giant renal angiomyolipoma: A case report
Tuberous sclerosis complex (TSC) is an autosomal dominant disease involving multiple organs, but there are a limited number of reports on family TSC. In the present report, a case of a 52-year-old female with a familial genetic TSC, associated with bilateral giant renal angiomyolipoma, was described. The mother, second elder brother and daughter of the patient all exhibited TSC, but the clinica...
متن کاملConcurrent hepatic and ruptured renal angiomyolipoma in tuberous sclerosis complex.
Angiomyolipoma of the liver or kidney is one of the clinical manifestations of tuberous sclerosis complex. However, concurrence of angiomyolipoma in both liver and kidney associated with tuberous sclerosis complex is a rare entity. Renal angiomyolipomas with large aneurysms confer a higher probability of rupture as compared to small aneurysms. Herein, we document a case of tuberous sclerosis co...
متن کاملEfficacy of Everolimus for Treating Renal Angiomyolipoma with Inferior Vena Cava Thrombus Associated with Tuberous Sclerosis: A Case Report
Here we report a case of 57-year-old woman with renal angiomyolipoma associated with tuberous sclerosis complex involving inferior vena cava thrombus. We could perform less invasive nephrectomy with thrombectomy because everolimus administration reduced the inferior vena cava thrombus. To the best of our knowledge, this is the first report the use of everolimus before performing surgery to trea...
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ژورنال
عنوان ژورنال: The Japanese Journal of Urology
سال: 2016
ISSN: 0021-5287,1884-7110
DOI: 10.5980/jpnjurol.107.54